Chordoma has been described as a rare malignant tumor derived from the primitive notochord involving the axial skeleton, characterized by a long clinical course, resistance to radiotherapy and a tendency to remain localized with infrequent metastasis. More than one third of chordoma occur at the base of the skull. Typical ventral extension of the neoplasm is in the direction of the nasopharynx and occasionally into the nasal cavity or maxillary antrum. Recently we experienced one case of the chordoma in the nasopharynx. A 5 year old male suffered from nasal obstruction and sneezing for 3 years. Extirpation was done and was proved as chordoma.