Rhabdomyosarcoma is the most common soft tissue sarcoma in children with an incidence of 0.2/100,000 children per year. Approximately 40% occur in the head and neck. The most common location is the orbit, followed by the nasopharynx and paranasal sinuses. The mode of spread is local extension, often with lymph node metastases. Distant metastases occurs most commonly to the lungs, bone, and bone marrow. The most favorable outcome occurs in those patients whose sarcoma can be totally resected. The use of radiation therapy and VAC(Vincristine, Actinomycin D, and Cyclophosphamide) chemotherapy has greatly enhanced curability. We experienced a case of embryonal rhabdomyosarcoma of the left cheek managed with complete excision, chemotherapy and radiation therapy.
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