Neurogenic tumor of the larynx is very rare disease and is mostly presented as neurofibroma or Schwannoma. These tumors are appeared in any age group, and less than 100 cases are reported in the world literature. Authors experienced a case of laryngeal neurofibroma occurring in a 2-month old boy with a presenting symptom of progressive stridor since the time of birth. It is our intention to present this case with literature review.